Xantogranuloma necrobiotico. Diagnostico diferencial, tratamiento e implicaciones sistemicas. A proposito de un caso.

Fecha de publicación:

Autores de IIS La Fe

  • Empar Sanz Marco

    Autor

  • María Jesus Lopez-Prats Lucea

    Autor

  • Melitina Chirivella Casanova

    Autor

  • Juan Aurelio Aviñó Martínez

    Autor

  • Manuel Díaz Llopis

    Autor

Abstract

CASE REPORT: A 48-year-old male was referred to our hospital for further evaluation of eyelid edema with bilateral yellowish ulcerated nodules. Suspecting a xanthogranulomatosis, imaging tests and biopsy were performed with diagnosis of necrobiotic xanthogranuloma. IgG monoclonal gammapathy was diagnosed in a systemic study. Systemic corticosteroids and cyclosporine were initiated unsuccessfully; therefore intra-lesional injections of triamcinolone were started, which controlled the orbital disease. DISCUSSION: Necrobiotic xanthogranuloma is a rare condition that usually affects the eyelids and anterior orbit. Its diagnosis is important as it is associated with malignant lymphoproliferative processes. Intra-lesional corticosteroids were effective in our patient.

Datos de la publicación

ISSN/ISSNe:
0365-6691, 1989-7286

Archivos de la Sociedad Espanola de Oftalmologia  Elsevier Ltd

Tipo:
Abstract of Published Item
Páginas:
186-189
PubMed:
24269389
Factor de Impacto:
0,230 SCImago
Cuartil:
Q3 SCImago

Documentos

  • No hay documentos

Métricas

Filiaciones

Filiaciones no disponibles

Keywords

  • Corticoides; Corticosteroids; Gammapatia monoclonal; Monoclonal gammapathy; Necrobiotic xanthogranuloma; Xanthogranuloma; Xanthogranulomatosis; Xantogranuloma; Xantogranuloma necrobiotico; Xantogranulomatosis

Cita

Compartir