Enteric duplication cysts in children: varied presentations, varied imaging findings

Fecha de publicación: 01/12/2018

Autores de IIS La Fe

• Cinta Sanguesa Nebot

  Autor

• Roberto Llorens Salvador

  Autor

• Maria Elena Carazo Palacios

  Autor

• Sandra Perez Aliaga

  Autor

• Vicente Ibáñez Pradas

  Autor

Grupos

• Hepatología experimental y Trasplante hepático

  Investigador Principal

  Laia Tolosa Pardo

• Investigacion Biomédica en Imagen (GIBI 2-30)

  Investigador Principal

  Leonor Cerdá Alberich

Abstract

Enteric duplication cysts (EDCs) are rare congenital malformations formed during the embryonic development of the digestive tract. They are usually detected prenatally or in the first years of life. The size, location, type, mucosal pattern and presence of complications produce a varied clinical presentation and different imaging findings. Ultrasonography (US) is the most used imaging method for diagnosis. Magnetic resonance (MR) and computed tomography (CT) are less frequently used, but can be helpful in cases of difficult surgical approach. Conservative surgery is the treatment of choice. Pathology confirms the intestinal origin of the cyst, showing a layer of smooth muscle in the wall and an epithelial lining inside, resembling some part of the gastrointestinal tract (GT). We review the different forms of presentation of the EDCs, showing both the typical and atypical imaging findings with the different imaging techniques. We correlate the imaging findings with the surgical results and the final pathological features.Teaching Points center dot EDCs are rare congenital anomalies from the digestive tract with uncertain pathogenesis.center dot More frequently, diagnosis is antenatal, with most EDCs occurring in the distal ileum.center dot Ultrasonography is the method of choice for diagnosis of EDCs.center dot Complicated EDCs can show atypical imaging findings.center dot Surgery is necessary to avoid complications.

Keywords

• Cyst; Gastrointestinal tract; Children; Ultrasound; Magnetic resonance