Portal de investigación
How strict is galactose restriction in adults with galactosaemia? International practice
Autores de IIS La Fe
Participantes ajenos a IIS La Fe
- Adam, S
- Akroyd, R
- Bernabei, S
- Bollhalder, S
- Boocock, S
- Burlina, A
- Coote, T
- Corthouts, K
- Dawson, S
- Defourny, S
- De Meyer, A
- Desloovere, A
- Devlin, Y
- Diels, M
- Dokoupil, K
- Donald, S
- Evans, S
- Fasan, I
- Ferguson, C
- Ford, S
- Forga, M
- Gallo, G
- Grunert, SC
- Heddrich-Ellerbrok, M
- Heidenborg, C
- Jonkers, C
- Lefebure, K
- Luyten, K
- MacDonald, A
- Meyer, U
- Micciche, A
- Muller, E
- Portnoi, P
- Ripley, S
- Robert, M
- Robertson, LV
- Rosenbaum-Fabian, S
- Sahm, K
- Schultz, S
- Singleton, K
- Sjoqvist, E
- Stoelen, L
- Terry, A
- Thompson, S
- Timmer, C
- Vande Kerckhove, K
- van der Ploeg, L
- Van Driessche, M
- van Rijn, M
- van Teeffelen-Heithoff, A
- Voillot, C
- Wenz, J
- Westbrook, M
- Wildgoose, J
- Zweers, H
Grupos
Abstract
Dietary management of 418 adult patients with galactosaemia (from 39 centres/12 countries) was compared. All centres advised lactose restriction, 6 restricted galactose from galactosides +/- fruits and vegetables and 12 offal. 38% (n = 15) relaxed diet by: 1) allowing traces of lactose in manufactured foods (n = 13) or 2) giving fruits, vegetables and galactosides (n = 2). Only 15% (n = 6) calculated dietary galactose. 32% of patients were lost to dietetic follow-up. In adult galactosaemia, there is limited diet relaxation. (C) 2015 Elsevier Inc. All rights reserved.
Datos de la publicación
- ISSN/ISSNe:
- 1096-7192, 1096-7206
- Tipo:
- Article
- Páginas:
- 23-26
- PubMed:
- 25873073
- Factor de Impacto:
- 1,541 SCImago ℠
- Cuartil:
- Q1 SCImago ℠
MOLECULAR GENETICS AND METABOLISM ACADEMIC PRESS INC ELSEVIER SCIENCE
Citas Recibidas en Web of Science: 9
Documentos
- No hay documentos
Filiaciones
Keywords
- Galactosaemia; Galactose; Lactose; Galactose-1-phosphate; Diet; Monitoring
Cita
Adam S,Akroyd R,Bernabei S,Bollhalder S,Boocock S,Burlina A,Coote T,Corthouts K,DALMAU J,Dawson S,Defourny S,De Meyer A,Desloovere A,Devlin Y,Diels M,Dokoupil K,Donald S,Evans S,Fasan I,Ferguson C,Ford S,Forga M,Gallo G,Grunert SC,Heddrich M,Heidenborg C,Jonkers C,Lefebure K,Luyten K,MacDonald A,Meyer U,Micciche A,Muller E,Portnoi P,Ripley S,Robert M,Robertson LV,Rosenbaum S,Sahm K,Schultz S,Singleton K,Sjoqvist E,Stoelen L,Terry A,Thompson S,Timmer C,Vande K,van der Ploeg L,Van M,van M,van Teeffelen A,VITORIA I,Voillot C,Wenz J,Westbrook M,Wildgoose J,Zweers H. How strict is galactose restriction in adults with galactosaemia? International practice. Mol. Genet. Metab. 2015. 115. (1):p. 23-26. IF:3,093. (2).