Rabdomiosarcoma alveolar orbitario enmascarado por sinusitis etmoidal en un adulto de 25 anos.

Autores de IIS La Fe

• Empar Sanz Marco

  Autor

• Enrique España Gregori

  Autor

• Judith Pérez Rojas

  Autor

• María Jesus Lopez-Prats Lucea

  Autor

• Manuel Díaz Llopis

  Autor

Participantes ajenos a IIS La Fe

• Alamar A

Grupos

• Hepatología, Cirugia Hepatobiliopancreática y Trasplantes

• Investigación en Neuroinmunología y Esclerosis Múltiple

Abstract

CASE REPORT: A 25-year-old woman with right subacute sinusitis, complained about discomfort in her right eye. Clinical manifestations and computed tomography were suggestive of sub-periosteal orbital ethmoid wall abscess, for which the patient underwent urgent drainage. A solid tumor was found, with a positive biopsy for alveolar rhabdomyosarcoma. Complete remission and resolution of orbital symptoms were achieved with chemotherapy and radiation therapy. DISCUSSION: Alveolar orbital rhabdomyosarcoma in adults is uncommon. Rhabdomyosarcoma has a high risk of spreading. It can simulate a sinusitis, as in our patient, early diagnosis and early treatment being especially important in these patients.

Keywords

• Apex; Masked orbital rhabdomyosarcoma; Rabdomiosarcoma; Rabdomiosarcoma alveolar; Rabdomiosarcoma orbitario enmascarado; Rhabdomyosarcoma; Rhabdomyosarcoma alveolar; Sinusitis; Apex